| 스테로이드 의존성 신증후군에서 진단된 Clq nephropathy 1례 |
| 이정원, 조수진, 이승주, 성순희 |
1이화여자대학교 의과대학 소아과학교실, 이화의과학연구소
2이화여자대학교 의과대학 소아과학교실, 이화의과학연구소
3이화여자대학교 의과대학 소아과학교실, 이화의과학연구소
4이화여자대학교 의과대학 병리학교실, 이화의과학연구소 |
| A Case of C1q Nephropathy in Steroid-Dependent Nephrotic Syndrome |
| Jung Won Lee, Su Jin Cho, Seoung Joo Lee, Soon Hee Sung |
1Department of Pediatrics, Ewha Womans University, College of Medicine, Ewha Medical Research Center
2Department of Pediatrics, Ewha Womans University, College of Medicine, Ewha Medical Research Center
3Department of Pediatrics, Ewha Womans University, College of Medicine, Ewha Medical Research Center
4Department of Pathology, Ewha Womans University, College of Medicine, Ewha Medical Research Center |
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| ABSTRACT |
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C1q nephropathy is an immune complex glomerulonephritis defined by the presence of mesangial C1q deposits in immunofluorescence microscopy and electron dense deposits on electron microscopy. It was described as a distinct disease entity in 1985 by Jennette and Hipp. Thirty four cases were reported in the literature but there has been no pediatric case reported in Korea yet. It commonly presents with steroid-resistent nephrotic syndrome in older children and young adults, and occasionally nephritic-nephrotic syndrome or rapidly progressive glomerulonephritis. We report a case of C1q nephropathy in a 23-month-old girl with steroid-dependent nephrotic syndrome. |
| Key words:
C1q nephropathy | Steroid-dependent nephrotic syndrome |
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