| 단측에 발생한 사구체낭성신질환 1례 |
| 오승진, 육진원, 김지홍, 정현주, 김명준, 김병길 |
1연세대학교 의과대학 소아과학교실 및 신장질환연구소
2연세대학교 의과대학 소아과학교실 및 신장질환연구소
3연세대학교 의과대학 소아과학교실 및 신장질환연구소
4연세대학교 의과대학 병리학교실 및 신장질환연구소
5연세대학교 의과대학 진단 방사선과학교실 및 신장질환연구소
6연세대학교 의과대학 소아과학교실 및 신장질환연구소 |
| A Case Report Unilaterally Involved Glomerulocystic Kidney Disease |
| Seung-Jin Oh, Jin-Won Yook, Ji-Hong Kim, Hyun-Ju Chung, Myung-Joon Kim, Pyung-Kil Kim |
1Departments of Pediatrics, and The Institute of Kidney Disease, Yonsei University College of Medicine
2Departments of Pediatrics, and The Institute of Kidney Disease, Yonsei University College of Medicine
3Departments of Pediatrics, and The Institute of Kidney Disease, Yonsei University College of Medicine
4Departments of Pathology, and The Institute of Kidney Disease, Yonsei University College of Medicine
5Departments of Radiology, and The Institute of Kidney Disease, Yonsei University College of Medicine
6Departments of Pediatrics, and The Institute of Kidney Disease, Yonsei University College of Medicine |
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| ABSTRACT |
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Glomerulocystic kidney disease(GCKD) is a rare form of renal cystic disease defined histopathologically by containing dilated Bowman's space with variable atrophy of glomerular tufts, which may occur as sporadically or as familial cases and can be presented as a major component of heritable syndromes. It has not been recognized in Korean children but only one report of adult case has been reported having GCKD. We experienced a case of GCKD in a 10-year-10-month-old boy, who was admitted for hypertension. Abdominal ultrasonography and computed tomography revealed clustered numerous small cysts in left kidney and renal biopsy findings was consistent with the GCKD showing cystic dilatation of Bowman's space with intact glomerular structure. |
| Key words:
Glomerulocystic kidney disease | Autosomal dominant polycystic kidney disease |
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