A Female Infant with Segmental Multicystic Dysplastic Kidney

Lee, Jun Ho; Kim, Moon Kyu

doi:2013.17.1.25

J Korean Soc Pediatr Nephrol > Volume 17(1); 2013 > Article

Case Report

J Korean Soc Pediatr Nephrol 2013;17(1): 25-28. doi: https://doi.org/10.3339/jkspn.2013.17.1.25

분절형 다낭성 이형성신 영아 보고 1례

이준호, 김문규

차의과학대학교 소아과학교실

A Female Infant with Segmental Multicystic Dysplastic Kidney

Jun Ho Lee, Moon Kyu Kim

Departments of Pediatrics, CHA Bundang Medical Center, CHA University, Seongnam, South Korea

Corresponding Author: Jun Ho Lee ,Tel: 031-780-5011, Fax: 031-780-5011, Email: naesusana@yahoo.co.kr

Received: October 27, 2012; Accepted: December 4, 2012.

This is an open-access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http:// creativecommons. org/licenses/bync/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

ABSTRACT

There have only been 35 pediatric cases and one adult case reported on segmental multicystic dysplastic kidney (MCDK) from our search in PubMed, including 19 cases detected antenatally. There is little documentation of segmental MCDK, particularly concerning its natural history. Segmental MCDK can be presented atypically, making diagnosis more difficult. We report an another case with segmental MCDK. Multicystic abdominal mass detected on antenatal sonogram in this infant was diagnosed as segmental MCDK by renal ultrasonography and computed tomography. If a definitive diagnosis of segmental MCDK can be made on imaging, surgery is not required for a diagnostic biopsy.

Key words: Computed tomography | Multicystic renal mass | Renal ultrasonography | Segmental multicystic dysplastic kidney