1Department of Pediatrics, Pusan Paik Hospital, Inje University, College of Medicine 2Department of Pediatrics, Pusan Paik Hospital, Inje University, College of Medicine 3Department of Pediatrics, Pusan Paik Hospital, Inje University, College of Medicine 4Department of Pediatrics, Pusan Paik Hospital, Inje University, College of Medicine
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ABSTRACT
Focal Segmental Glomerulosclerosis(FSGS) is one of the underlying pathology of congenital and infantile nephrotic syndrome. There is no ultimate curative treatment except renal transplantation. We have experienced a case of infantile nephrotic syndrome In a 10 month old boy who presented with proteinuria and hematuria. His elder brother also suffered from nephrotic syndrome and died at the age of 18 months due to sepsis. We have diagnosed this patient with clinical manifestations, laboratory data and pathologic findings which was done by open renal biopsy. The patient expired 54 days after admission because or progressive uremia and sepsis.